Title |
ANCA-associated Vasculitis Presenting as Severe Pulmonary Hypertension and Right Heart Failure
|
---|---|
Published in |
Indian Journal of Pediatrics, June 2017
|
DOI | 10.1007/s12098-017-2379-0 |
Pubmed ID | |
Authors |
Rakesh Kumar Pilania, Sumeet R. Dhawan, Joseph L. Mathew, Surjit Singh, K. S. Sodhi, Meenu Singh |
Abstract |
Microscopic polyangiitis (MPA) is a small vessel multisystemic disorder characterised by necrotising small vessel vasculitis without any immune deposits. Kidney and lung are the predominant organs affected in MPA. Skin, gastrointestinal and neurological findings are also described. Isolated pulmonary manifestations are rare. The authors describe a two-year girl who presented with right heart failure and was subsequently diagnosed as ANCA-associated vasculitis. This case report is intended to sensitise pediatricians to consider systemic vasculitis with pulmonary hemorrhage in children with pulmonary hypertension even in the absence of severe pallor. |
X Demographics
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 2 | 100% |
Demographic breakdown
Type | Count | As % |
---|---|---|
Members of the public | 2 | 100% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 13 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Student > Doctoral Student | 2 | 15% |
Researcher | 2 | 15% |
Librarian | 1 | 8% |
Student > Bachelor | 1 | 8% |
Unknown | 7 | 54% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 3 | 23% |
Immunology and Microbiology | 1 | 8% |
Agricultural and Biological Sciences | 1 | 8% |
Unknown | 8 | 62% |