Title |
Autosomal recessive polycystic kidney disease and congenital hepatic fibrosis (ARPKD/CHF)
|
---|---|
Published in |
Pediatric Radiology, December 2008
|
DOI | 10.1007/s00247-008-1064-x |
Pubmed ID | |
Authors |
Baris Turkbey, Iclal Ocak, Kailash Daryanani, Esperanza Font-Montgomery, Linda Lukose, Joy Bryant, Maya Tuchman, Parvathi Mohan, Theo Heller, William A. Gahl, Peter L. Choyke, Meral Gunay-Aygun |
Abstract |
ARPKD/CHF is an inherited disease characterized by non-obstructive fusiform dilatation of the renal collecting ducts leading to enlarged spongiform kidneys and ductal plate malformation of the liver resulting in congenital hepatic fibrosis. ARPKD/CHF has a broad spectrum of clinical presentations involving the kidney and liver. Imaging plays an important role in the diagnosis and follow-up of ARPKD/CHF. Combined use of conventional and high-resolution US with MR cholangiography in ARPKD/CHF patients allows detailed definition of the extent of kidney and hepatobiliary manifestations without requiring ionizing radiation and contrast agents. |
X Demographics
Geographical breakdown
Country | Count | As % |
---|---|---|
United States | 2 | 100% |
Demographic breakdown
Type | Count | As % |
---|---|---|
Members of the public | 1 | 50% |
Scientists | 1 | 50% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Japan | 1 | 1% |
Germany | 1 | 1% |
Unknown | 71 | 97% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Other | 13 | 18% |
Student > Ph. D. Student | 8 | 11% |
Researcher | 8 | 11% |
Student > Bachelor | 7 | 10% |
Student > Doctoral Student | 6 | 8% |
Other | 18 | 25% |
Unknown | 13 | 18% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 38 | 52% |
Biochemistry, Genetics and Molecular Biology | 6 | 8% |
Agricultural and Biological Sciences | 5 | 7% |
Linguistics | 1 | 1% |
Nursing and Health Professions | 1 | 1% |
Other | 4 | 5% |
Unknown | 18 | 25% |