Title |
Pseudotumor cerebri in kaposiform lymphangiomatosis: a case report and pathogenetic hypothesis
|
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Published in |
Child's Nervous System, April 2018
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DOI | 10.1007/s00381-018-3794-x |
Pubmed ID | |
Authors |
Cristina Barceló-López, Antonio L. López-Guerrero, Antonio García-López, José Hurtado-Marín, Helena Alarcón-Martínez, Juan F. Martínez-Lage |
Abstract |
A 4-year-old boy with kaposiform lymphangiomatosis (KLA) developed progressive headaches and papilloedema and was diagnosed with pseudotumor cerebri initially treated with acetazolamide. Clinical deterioration prompted placement of a ventriculoperitoneal shunt. After the surgery, the child's condition has markedly improved. A network of intracranial lymphatics is presently being investigated. Neuroimaging excluded KLA infiltration of the skull and/or meninges, leaving as the most plausible explanation for the child's pseudotumor cerebri the existence of an increase in intracranial venous pressure by venous compression at the thorax. To our knowledge, our case constitutes the first report of pseudotumor cerebri occurring in the context of KLA. |
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United States | 1 | 50% |
Spain | 1 | 50% |
Demographic breakdown
Type | Count | As % |
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Science communicators (journalists, bloggers, editors) | 1 | 50% |
Members of the public | 1 | 50% |
Mendeley readers
Geographical breakdown
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Unknown | 10 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
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Student > Doctoral Student | 2 | 20% |
Other | 2 | 20% |
Lecturer > Senior Lecturer | 1 | 10% |
Librarian | 1 | 10% |
Student > Bachelor | 1 | 10% |
Other | 1 | 10% |
Unknown | 2 | 20% |
Readers by discipline | Count | As % |
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Medicine and Dentistry | 5 | 50% |
Pharmacology, Toxicology and Pharmaceutical Science | 1 | 10% |
Physics and Astronomy | 1 | 10% |
Immunology and Microbiology | 1 | 10% |
Unknown | 2 | 20% |