Title |
Chediak-Higashi Syndrome and Premature Exfoliation of Primary Teeth
|
---|---|
Published in |
Brazilian Dental Journal, December 2013
|
DOI | 10.1590/0103-6440201302258 |
Pubmed ID | |
Authors |
Karla Mayra Rezende, Alfredo Hiram Carrillo Canela, Adriana Oliveira Lira Ortega, Claudia Tintel, Marcelo Bönecker |
Abstract |
The Chediak-Higashi syndrome (CHS) is a rare hereditary fatal disease, if not treated. These changes are associated with various diseases and syndromes that mainly cause periodontal disease and thus the premature loss of teeth. This paper describes the monitoring of premature loss of primary teeth that began when the child was 5 years old. On presentation his teeth were mobile and there was a history of gingival bleeding. Panoramic radiography revealed generalized and severe bone loss, and the teeth showed no bony support enough for their stability. Blood test was ordered to assess the overall health of the child and giant cells with cytoplasmic granules were found, confirming the diagnosis of CHS. The management of periodontal disease focused on the control of infection and bacterial plaque by mechanical and chemical methods. |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 57 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Student > Master | 12 | 21% |
Student > Bachelor | 6 | 11% |
Student > Postgraduate | 6 | 11% |
Other | 5 | 9% |
Student > Doctoral Student | 4 | 7% |
Other | 9 | 16% |
Unknown | 15 | 26% |
Readers by discipline | Count | As % |
---|---|---|
Medicine and Dentistry | 32 | 56% |
Agricultural and Biological Sciences | 5 | 9% |
Biochemistry, Genetics and Molecular Biology | 2 | 4% |
Nursing and Health Professions | 1 | 2% |
Decision Sciences | 1 | 2% |
Other | 3 | 5% |
Unknown | 13 | 23% |