Title |
Behçet disease in association with Budd-Chiari syndrome and multiple thrombosis - Case report
|
---|---|
Published in |
Anais Brasileiros de Dermatologia, June 2013
|
DOI | 10.1590/abd1806-4841.20131930 |
Pubmed ID | |
Authors |
Maraya de Jesus Semblano Bittencourt, Carolina Moraes Dias, Thaiane Lima Lage, Renata Silva Barros, Otavio Augusto Gomes Paz, Waldonio de Brito Vieira |
Abstract |
Behçet's disease is a chronic inflammatory disease of unknown aetiology, characterized by recurrent oral and genital aphthous ulcerations, uveitis, skin lesions and other multisystem affections associated with vasculitis. Different types of vessels, predominantly veins, can be affected in Behçet's disease. The frequency of vascular lesions in Behçet's disease, such as superficial and deep venous thromboses, arterial aneurysms and occlusions, ranges between 7-29%. Budd-Chiari syndrome is a rare and serious complication of Behçet's disease and implies thrombosis of the hepatic veins and/or the intrahepatic or suprahepatic inferior vena cava. We report a case of a 25-year-old man with Behçet's disease that developed Budd-Chiari syndrome. The correlation of dermatological, pathological and imaging studies confirmed the diagnosis. |
X Demographics
Geographical breakdown
Country | Count | As % |
---|---|---|
Spain | 1 | 50% |
Unknown | 1 | 50% |
Demographic breakdown
Type | Count | As % |
---|---|---|
Members of the public | 2 | 100% |
Mendeley readers
Geographical breakdown
Country | Count | As % |
---|---|---|
Unknown | 3 | 100% |
Demographic breakdown
Readers by professional status | Count | As % |
---|---|---|
Student > Doctoral Student | 1 | 33% |
Unknown | 2 | 67% |
Readers by discipline | Count | As % |
---|---|---|
Nursing and Health Professions | 1 | 33% |
Unknown | 2 | 67% |