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Neurodegenerative Diseases

Overview of attention for book
Cover of 'Neurodegenerative Diseases'

Table of Contents

  1. Altmetric Badge
    Book Overview
  2. Altmetric Badge
    Chapter 1 Acuted Disseminated Encephalomyelitis
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    Chapter 2 Age-Related Macular Degeneration
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    Chapter 3 Arachnoid Cysts
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    Chapter 4 Autism Spectrum Disorders: Information for Pediatricians Supporting Families of Young Children on the Spectrum
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    Chapter 5 Autosomal Recessive Charcot-Marie-Tooth Neuropathy
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    Chapter 6 Creutzfeldt-Jakob disease.
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    Chapter 7 Epigenetics in autism and other neurodevelopmental diseases.
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    Chapter 8 Epilepsy and Epileptic Syndrome
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    Chapter 9 Frontotemporal Lobar Degeneration.
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    Chapter 10 Neurodegenerative Diseases
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    Chapter 11 Juvenile Neuronal Ceroid Lipofuscinoses
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    Chapter 12 Neurodegenerative Diseases
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    Chapter 13 Leukodystrophies
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    Chapter 14 Machado-Joseph Disease and other Rare Spinocerebellar Ataxias.
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    Chapter 15 Neurodegenerations induced by organophosphorous compounds.
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    Chapter 16 Mitochondrial Importance in Alzheimer’s, Huntington’s and Parkinson’s Diseases
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    Chapter 17 Multiple sclerosis.
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    Chapter 18 Myotonic Dystrophy Type 1 or Steinert’s Disease
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    Chapter 19 Neurodegeneration in diabetes mellitus.
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    Chapter 20 Neurofibromatoses
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    Chapter 21 Oxidative stress in developmental brain disorders.
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    Chapter 22 Oxidative Stress and Mitochondrial Dysfunction in Down Syndrome
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    Chapter 23 Pick’s Disease
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    Chapter 24 Premature Aging Syndrome
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    Chapter 25 The savant syndrome and its possible relationship to epilepsy.
  27. Altmetric Badge
    Chapter 26 Sjogren-Larsson Syndrome
  28. Altmetric Badge
    Chapter 27 The spinocerebellar ataxias: clinical aspects and molecular genetics.
  29. Altmetric Badge
    Chapter 28 Tourette syndrome.
Attention for Chapter 14: Machado-Joseph Disease and other Rare Spinocerebellar Ataxias.
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About this Attention Score

  • Above-average Attention Score compared to outputs of the same age (55th percentile)
  • Good Attention Score compared to outputs of the same age and source (76th percentile)

Mentioned by

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3 tweeters

Citations

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14 Dimensions

Readers on

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41 Mendeley
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Chapter title
Machado-Joseph Disease and other Rare Spinocerebellar Ataxias.
Chapter number 14
Book title
Neurodegenerative Diseases
Published in
Advances in experimental medicine and biology, January 2012
DOI 10.1007/978-1-4614-0653-2_14
Pubmed ID
Book ISBNs
978-1-4614-0652-5, 978-1-4614-0653-2
Authors

Antoni Matilla-Dueñas

Abstract

The spinocerebellar ataxias (SCAs) are a group of neurodegenerative diseases characterised by progressive lack of motor coordination leading to major disability. SCAs show high clinical, genetic, molecular and epidemiological variability. In the last one decade, the intensive scientific research devoted to the SCAs is resulting in clear advances and a better understanding on the genetic and nongenetic factors contributing to their pathogenesis which are facilitating the diagnosis, prognosis and development of new therapies. The scope of this chapter is to provide an updated information on Machado-Joseph disease (MJD), the most frequent SCA subtype worldwide and other rare spinocerebellar ataxias including dentatorubral-pallidoluysian atrophy (DRPLA), the X-linked fragile X tremor and ataxia syndrome (FXTAS) and the nonprogressive episodic forms of inherited ataxias (EAs). Furthermore, the different therapeutic strategies that are currently being investigated to treat the ataxia and non-ataxia symptoms in SCAs are also described.

Twitter Demographics

The data shown below were collected from the profiles of 3 tweeters who shared this research output. Click here to find out more about how the information was compiled.

Mendeley readers

The data shown below were compiled from readership statistics for 41 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
Germany 2 5%
Chile 1 2%
Unknown 38 93%

Demographic breakdown

Readers by professional status Count As %
Student > Master 7 17%
Student > Bachelor 6 15%
Researcher 6 15%
Professor 4 10%
Other 3 7%
Other 12 29%
Unknown 3 7%
Readers by discipline Count As %
Medicine and Dentistry 15 37%
Neuroscience 7 17%
Agricultural and Biological Sciences 6 15%
Biochemistry, Genetics and Molecular Biology 2 5%
Social Sciences 1 2%
Other 4 10%
Unknown 6 15%

Attention Score in Context

This research output has an Altmetric Attention Score of 2. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 12 April 2012.
All research outputs
#4,260,447
of 8,847,334 outputs
Outputs from Advances in experimental medicine and biology
#977
of 2,761 outputs
Outputs of similar age
#38,723
of 94,524 outputs
Outputs of similar age from Advances in experimental medicine and biology
#5
of 26 outputs
Altmetric has tracked 8,847,334 research outputs across all sources so far. This one is in the 49th percentile – i.e., 49% of other outputs scored the same or lower than it.
So far Altmetric has tracked 2,761 research outputs from this source. They receive a mean Attention Score of 3.4. This one has gotten more attention than average, scoring higher than 61% of its peers.
Older research outputs will score higher simply because they've had more time to accumulate mentions. To account for age we can compare this Altmetric Attention Score to the 94,524 tracked outputs that were published within six weeks on either side of this one in any source. This one has gotten more attention than average, scoring higher than 55% of its contemporaries.
We're also able to compare this research output to 26 others from the same source and published within six weeks on either side of this one. This one has done well, scoring higher than 76% of its contemporaries.