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Cognitive development in patients with Mucopolysaccharidosis type III (Sanfilippo syndrome)

Overview of attention for article published in Orphanet Journal of Rare Diseases, June 2011
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1 X user

Citations

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Title
Cognitive development in patients with Mucopolysaccharidosis type III (Sanfilippo syndrome)
Published in
Orphanet Journal of Rare Diseases, June 2011
DOI 10.1186/1750-1172-6-43
Pubmed ID
Authors

Marlies J Valstar, Jan Pieter Marchal, Martha Grootenhuis, Vivian Colland, Frits A Wijburg

Abstract

Mucopolysaccharidosis type III (MPS III, Sanfilippo syndrome) is a lysosomal storage disorder caused by a deficiency of one of the enzymes involved in the degradation of heparan sulfate. MPS III is characterized by progressive mental deterioration resulting in severe dementia. A number of potentially disease-modifying therapies are studied. As preservation of cognitive function is the ultimate goal of treatment, assessment of cognitive development will be essential in order to evaluate treatment efficacy. However, no large scale studies on cognitive levels in MPS III patients, using formal psychometric tests, have been reported.

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The data shown below were collected from the profile of 1 X user who shared this research output. Click here to find out more about how the information was compiled.
Mendeley readers

Mendeley readers

The data shown below were compiled from readership statistics for 73 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
Netherlands 1 1%
United Kingdom 1 1%
Denmark 1 1%
Spain 1 1%
United States 1 1%
Unknown 68 93%

Demographic breakdown

Readers by professional status Count As %
Researcher 14 19%
Student > Master 11 15%
Student > Bachelor 8 11%
Student > Ph. D. Student 7 10%
Other 5 7%
Other 14 19%
Unknown 14 19%
Readers by discipline Count As %
Medicine and Dentistry 17 23%
Agricultural and Biological Sciences 15 21%
Psychology 9 12%
Biochemistry, Genetics and Molecular Biology 5 7%
Neuroscience 3 4%
Other 8 11%
Unknown 16 22%
Attention Score in Context

Attention Score in Context

This research output has an Altmetric Attention Score of 1. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 06 March 2012.
All research outputs
#20,155,513
of 22,663,150 outputs
Outputs from Orphanet Journal of Rare Diseases
#2,436
of 2,590 outputs
Outputs of similar age
#106,170
of 114,655 outputs
Outputs of similar age from Orphanet Journal of Rare Diseases
#7
of 7 outputs
Altmetric has tracked 22,663,150 research outputs across all sources so far. This one is in the 1st percentile – i.e., 1% of other outputs scored the same or lower than it.
So far Altmetric has tracked 2,590 research outputs from this source. They typically receive a little more attention than average, with a mean Attention Score of 7.4. This one is in the 1st percentile – i.e., 1% of its peers scored the same or lower than it.
Older research outputs will score higher simply because they've had more time to accumulate mentions. To account for age we can compare this Altmetric Attention Score to the 114,655 tracked outputs that were published within six weeks on either side of this one in any source. This one is in the 1st percentile – i.e., 1% of its contemporaries scored the same or lower than it.
We're also able to compare this research output to 7 others from the same source and published within six weeks on either side of this one.