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Cognitive development in patients with Mucopolysaccharidosis type III (Sanfilippo syndrome)

Overview of attention for article published in Orphanet Journal of Rare Diseases, June 2011
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1 tweeter

Citations

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Title
Cognitive development in patients with Mucopolysaccharidosis type III (Sanfilippo syndrome)
Published in
Orphanet Journal of Rare Diseases, June 2011
DOI 10.1186/1750-1172-6-43
Pubmed ID
Authors

Marlies J Valstar, Jan Pieter Marchal, Martha Grootenhuis, Vivian Colland, Frits A Wijburg

Abstract

Mucopolysaccharidosis type III (MPS III, Sanfilippo syndrome) is a lysosomal storage disorder caused by a deficiency of one of the enzymes involved in the degradation of heparan sulfate. MPS III is characterized by progressive mental deterioration resulting in severe dementia. A number of potentially disease-modifying therapies are studied. As preservation of cognitive function is the ultimate goal of treatment, assessment of cognitive development will be essential in order to evaluate treatment efficacy. However, no large scale studies on cognitive levels in MPS III patients, using formal psychometric tests, have been reported.

Twitter Demographics

The data shown below were collected from the profile of 1 tweeter who shared this research output. Click here to find out more about how the information was compiled.

Mendeley readers

The data shown below were compiled from readership statistics for 69 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
Netherlands 1 1%
United Kingdom 1 1%
Denmark 1 1%
Spain 1 1%
United States 1 1%
Unknown 64 93%

Demographic breakdown

Readers by professional status Count As %
Researcher 14 20%
Student > Master 11 16%
Student > Bachelor 9 13%
Student > Ph. D. Student 7 10%
Other 5 7%
Other 15 22%
Unknown 8 12%
Readers by discipline Count As %
Medicine and Dentistry 17 25%
Agricultural and Biological Sciences 15 22%
Psychology 9 13%
Biochemistry, Genetics and Molecular Biology 5 7%
Neuroscience 3 4%
Other 10 14%
Unknown 10 14%

Attention Score in Context

This research output has an Altmetric Attention Score of 1. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 06 March 2012.
All research outputs
#4,207,687
of 5,039,474 outputs
Outputs from Orphanet Journal of Rare Diseases
#770
of 858 outputs
Outputs of similar age
#65,272
of 79,213 outputs
Outputs of similar age from Orphanet Journal of Rare Diseases
#10
of 10 outputs
Altmetric has tracked 5,039,474 research outputs across all sources so far. This one is in the 1st percentile – i.e., 1% of other outputs scored the same or lower than it.
So far Altmetric has tracked 858 research outputs from this source. They receive a mean Attention Score of 4.3. This one is in the 1st percentile – i.e., 1% of its peers scored the same or lower than it.
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