Defects of Secretion in Cystic Fibrosis

Chapter 1 Outside neurons/inside epithelia: Novel activation of CFTR CL- and HCO3 - conductances

Chapter 2 Role of CFTR and Other Ion Channels in Cystic Fibrosis

Chapter 3 Ion Channels in the Apical Membrane: Role of Electrical Coupling on Transepithelial Transport

Chapter 4 Ion Channels in Secretory Granules of the Pancreas: Molecular Identification and Their Role in Regulated Secretion

Chapter 5 Epithelial Transport and Intracellular Trafficking: Physiology and Pathophysiology

Chapter 6 Kinases, Cell Volume, and the Regulation of Chloride Channels

Chapter 7 The CLCAs: Proteins with Ion Channel, Cell Adhesion and Tumor Suppressor Functions

Chapter 8 Is Intervention in Inositol Phosphate Signaling a Useful Therapeutic Option for Cystic Fibrosis?

Chapter 9 An Inositol Phosphate Analog, INO-4995, Normalizes Electrophysiology in CF Airway Epithelia

Chapter 11 Airway Glycoconjugates Secreted in Cystic Fibrosis and Severe Chronic Airway Inflammation Relationship with Pseudomonas aeruginosa

Chapter 12 Biosynthesis and Secretion of Mucins, Especially the MUC2 Mucin, in Relation to Cystic Fibrosis